A case of atypical progressive cribriform and zosteriform hyperpigmentation

We report a case of atypical progressive cribriform and zosteriform hyperpigmentation (PCZH) in a 4-year-old boy. Progressive cribriform and zosteriform hyperpigmentation is a distinctive pigmentary disorder first described by Rower et al. in 1978. It is characterized clinically by uniformly tan cribriform macular pigmentation in a zosteriform distribution and histopathologically by increased melanin in the basal cell layer and absence of nevus cells. This case has two distinctive findings; the onset age was below 10 years and the lesions distributed on the whole body along Blaschko's lines. Histopathologic examination showed pigmentary incontinence.