Frosted branch angiitis, presumably related to dermatomyositis

Purpose: To report the first case of frosted branch angiitis associated with dermatomyositis in a Korean woman. Methods: Case report. Results: A 42-year-old woman with history of dermatomyositits presented with unilateral decreased visual acuity. Fundus examination showed findings consistent with frosted branch angiits. After 1 month of oral prednisolone, the patient made significant visual recovery with near complete resolution of vascular sheathing. Conclusions: To the best of the authors' knowledge, this is the first case of frosted branch angiitis associated with dermatomyositis. Dermatomyositis should be considered in the differential diagnosis of patients presenting with frosted branch angiitis.